Friday,
9 November 2007, 1:00pm
Kohlmeier-Degos
Disease (malignant atrophic papulosis) and Buerger’s Disease
(thromboangiitis obliterans) are conditions characterized by minimally
inflammatory obstruction of medium and small blood vessels. Damage
results when tissues are deprived of their blood supply (mostly
skin, brain and intestines in Degos; distal extremities in Buerger's).
Degos usually presents with a characteristic atrophic papular rash
(seen here at right). These diseases are often difficult to diagnose,
and treatment options are limited. This First International Medical,
Scientific and Patient Conference will explore their pathophysiology
and treatment, with an opportunity to see the human side of Degos
disease.
~~~
Program
The afternoon
session will be held in the Ether Dome, 4th Floor of the Bulfinch
Bldg, Massachusetts General Hospital in downtown Boston, Massachusetts,
USA
Welcome
1:00pm Richard Chou MD PhD, Massachusetts General
Hospital Rheumatology
Dermatologic
manifestations
1:10pm Noah Scheinfeld MD, Overview, Columbia
University Dermatology
1:50pm Bonnie Mackool MD, Differential diagnosis, Massachusetts
General Hospital Dermatology
2:00pm Marty Mihm MD, Dermatologic pathology, Massachusetts
General Hospital Pathology
2:15pm Discussion
Families
will move to the alternate program for patients, Bulfinch Bldg third
floor.
2:30pm
Brian Tseng MD, Perspectives on Family-sponsored Research, MGH
CF Center
3:00pm Paula Rauch MD, Grappling with Chronic Disease, Massachusetts
General Hospital Child Psychiatry
3:30pm Judith Calder, Historical perspective on fighting Degos disease,
www.DegosDisease.com
4:00pm Heather Diskin MD, family case presentations
Pathology
and imaging:
2:30pm Matthew Frosch MD PhD, GI and Neuropathology, Massachusetts
General Hospital Pathology
2:50pm Raghu Amaravadi MD, Abdominal Imaging in Degos, Lahey
Clinic Dept of Radiology
3:10pm Ellen Grant MD, Neuroimaging in Degos, Chair,
MGH Pediatric Radiology
3:30pm Break
Systemic
disease considerations, and approaches to basic science research:
3:45pm Sosa V. Kocheril MBBS, Clinical Manifestations Mimicking
Vasculitis, Univ of Michigan Rheumatology
4:05pm Verne Caviness MD DPhil, Neurologic Degos Disease, MGH
Pediatric Neurology
4:25pm Constantine Stratakis MD DSc, Approaches to pathogenesis,
Program Director, NIH Pediatric Endocrinology
Patient reflections, clinical heterogeneity:
4:40pm Patient families rejoin other participants in the Ether Dome.
Judith Calder, Director of Degos Disease Foundation
Sandra Clancy Kaczmarek, Family Liaison, MGH Coordinated Care Clinic
5:15pm
Buffet Dinner, Bulfinch Bldg Third Floor
6:15pm Bus to Boston Convention Center
ACR
Study Group on Degos Disease, Thromboangiitis Obliterans, and Related
Vasculopathies
American College of Rheumatology Annual Meeting, Boston
Convention Center Rm 153
Moderator:
Patrick Whelan MD PhD, MassGeneral Hospital for
Children Rheumatology
7:45pm
Introduction
7:55pm John H. Stone MD MPH, Buerger’s Disease and Related
Vasculopathies
Up-to-Date, Rheumatology Editor; Massachusetts
General Hospital Rheumatology
8:20pm Athanasios Theodoridis MD, Basic Research on Degos Disease
Hautklinik und Immunologisches Zentrum, Dessau
Germany
8:45pm Noah S. Scheinfeld MD JD, Parallel Diseases and Degos Pathophysiology
Columbia Univ Dermatology
9:05pm Question & Answer
~~~
Sponsored by the Division
of Pediatric Rheumatology,
MassGeneral Hospital for Children; and by the Division
of Rheumatology, Allergy & Immunology, MGH Department
of Medicine
~~~
Attendees may claim up to six hours of Category
2 credit for continuing medical education purposes
~~~
The afternoon session is supported in part by
an unrestricted educational grant from Abbott Laboratories |